A81.1 Subacute sclerosing panencephalitis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Dawson's inclusion body encephalitis
• Van Bogaert's sclerosing leukoencephalopathy

Applies from A81 Atypical virus infections of central nervous system

Includes

• diseases of the central nervous system caused by prions

Use additional code

• code, if applicable, to identify:
• dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
• dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
• dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
• dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
• dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
• mild neurocognitive disorder due to known physiological condition (F06.7-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 127 — Dementia, Mild or Unspecified
• RxHCC V08: HCC 112 — Dementia, Except Alzheimer's Disease
• ESRD V24: HCC 52

MS-DRG index

Defines the logic of DRG(s) 056-057 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 046.2 Subacute sclerosing panencephalitis

Code annotations containing back-references to A81.1

Back-references to A81.1

• Type 1 Excludes: B05 Measles ("subacute sclerosing panencephalitis (A81.1)")

Diagnosis Index entries for A81.1

• Bodechtel-Guttman disease (subacute sclerosing panencephalitis)
• Dawson's (inclusion body) encephalitis
• Disease, diseased › Bodechtel-Guttmann (subacute sclerosing panencephalitis)
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › Dawson's (inclusion body)
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › diffuse sclerosing
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › inclusion body
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › subacute sclerosing
• Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › van Bogaert's
• Leukoencephalitis › subacute sclerosing
• Leukoencephalitis › van Bogaert's (sclerosing)
• Leukoencephalopathy › van Bogaert's (sclerosing)
• Panencephalitis, subacute, sclerosing
• Van Bogaert's leukoencephalopathy (sclerosing) (subacute)

Nearby codes

• A81 Atypical virus infections of central nervous system
• A81.0 Creutzfeldt-Jakob disease
• A81.00 Creutzfeldt-Jakob disease, unspecified
• A81.01 Variant Creutzfeldt-Jakob disease
• A81.09 Other Creutzfeldt-Jakob disease
• A81.1 Subacute sclerosing panencephalitis (this code)
• A81.2 Progressive multifocal leukoencephalopathy
• A81.8 Other atypical virus infections of central nervous system
• A81.81 Kuru
• A81.82 Gerstmann-Straussler-Scheinker syndrome
• A81.83 Fatal familial insomnia