C00.2 Malignant neoplasm of external lip, unspecified

Billable ICD-10-CM code, FY2026.

Applicable to

• Malignant neoplasm of vermilion border of lip NOS

Applies from C00 Malignant neoplasm of lip

Excludes1 (never code together)

• malignant melanoma of lip (C43.0)
• Merkel cell carcinoma of lip (C4A.0)
• other and unspecified malignant neoplasm of skin of lip (C44.0-)

Use additional code

• code to identify:
• alcohol abuse and dependence (F10.-)
• history of tobacco dependence (Z87.891)
• tobacco dependence (F17.-)
• tobacco use (Z72.0)

MS-DRG index

Defines the logic of DRG(s) 011-013 in MDC PRE.

Approximate ICD-9-CM (GEMs)

• 140.9 Malignant neoplasm of lip, unspecified, vermilion border (approximate)

Code annotations containing back-references to C00.2

Back-references to C00.2

• Type 1 Excludes: C43.0 Malignant melanoma of lip ("malignant neoplasm of vermilion border of lip (C00.0-C00.2)")
• Type 1 Excludes: C4A.0 Merkel cell carcinoma of lip ("malignant neoplasm of vermilion border of lip (C00.0-C00.2)")

Back-references to C00

• Type 1 Excludes: C44.0 Other and unspecified malignant neoplasm of skin of lip ("malignant neoplasm of lip (C00.-)")
• Code Also: D59.39 Other hemolytic-uremic syndrome ("malignant neoplasm (C00-C96)")
• Code First: D63.0 Anemia in neoplastic disease ("neoplasm (C00-D49)")
• Code First: D84.81 Immunodeficiency due to conditions classified elsewhere ("malignant neoplasms (C00-C96)")
• Code First: E08 Diabetes mellitus due to underlying condition ("malignant neoplasm (C00-C96)")
• Code First: G13.0 Paraneoplastic neuromyopathy and neuropathy ("underlying neoplasm (C00-D49)")
• Code First: G13.1 Other systemic atrophy primarily affecting central nervous system in neoplastic disease ("underlying neoplasm (C00-D49)")
• Code First: G32.8 Other specified degenerative disorders of nervous system in diseases classified elsewhere ("cerebral degeneration (due to) neoplasm (C00-D49)")
• Code First: G32.81 Cerebellar ataxia in diseases classified elsewhere ("cerebellar ataxia (in) neoplastic disease (paraneoplastic cerebellar degeneration) (C00-D49)")
• Code First: G53 Cranial nerve disorders in diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: G55 Nerve root and plexus compressions in diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: G73.1 Lambert-Eaton syndrome in neoplastic disease ("underlying neoplasm (C00-D49)")
• Code First: G73.3 Myasthenic syndromes in other diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: G91.4 Hydrocephalus in diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: G99.2 Myelopathy in diseases classified elsewhere ("neoplasm (C00-D49)")
• Code First: I31.31 Malignant pericardial effusion in diseases classified elsewhere ("underlying neoplasm (C00-D49)")
• Code First: J91.0 Malignant pleural effusion ("underlying neoplasm (C00-D49)")
• Code First: M36.0 Dermato(poly)myositis in neoplastic disease ("underlying neoplasm (C00-D49)")
• Code First: Z15.0 Genetic susceptibility to malignant neoplasm (", if applicable, any current malignant neoplasm (C00-C75, C81-C96)")

Nearby codes

• C00 Malignant neoplasm of lip
• C00.0 Malignant neoplasm of external upper lip
• C00.1 Malignant neoplasm of external lower lip
• C00.2 Malignant neoplasm of external lip, unspecified (this code)
• C00.3 Malignant neoplasm of upper lip, inner aspect
• C00.4 Malignant neoplasm of lower lip, inner aspect
• C00.5 Malignant neoplasm of lip, unspecified, inner aspect
• C00.6 Malignant neoplasm of commissure of lip, unspecified
• C00.8 Malignant neoplasm of overlapping sites of lip