D47.Z2 Castleman disease

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Excludes2 (not included here)

• Kaposi's sarcoma (C46.-)

Code also

• , if applicable, human herpesvirus 8 infection (B10.89)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 21 — Lymphoma and Other Cancers
• CMS-HCC V22: HCC 48 — Coagulation Defects and Other Specified Hematological Disorders
• RxHCC V08: HCC 21 — Lymphomas and Other Hematologic Cancers
• ESRD V24: HCC 48

MS-DRG index

Defines the logic of DRG(s) 820-822 in MDC 17.

Approximate ICD-9-CM (GEMs)

• 238.79 Other lymphatic and hematopoietic tissues (approximate)

Diagnosis Index entries for D47.Z2

• Disease, diseased › Castleman (unicentric) (multicentric)
• Disease, diseased › Castleman (unicentric) (multicentric) › HHV-8-associated

Nearby codes

• D47.2 Monoclonal gammopathy
• D47.3 Essential (hemorrhagic) thrombocythemia
• D47.4 Osteomyelofibrosis
• D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
• D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
• D47.Z2 Castleman disease (this code)
• D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
• D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified