E20.1 Pseudohypoparathyroidism

Billable ICD-10-CM code, FY2026.

Applies from E20 Hypoparathyroidism

Excludes1 (never code together)

• Di George's syndrome (D82.1)
• postprocedural hypoparathyroidism (E89.2)
• tetany NOS (R29.0)
• transitory neonatal hypoparathyroidism (P71.4)

MS-DRG index

Defines the logic of DRG(s) 640-641 in MDC 10.

Approximate ICD-9-CM (GEMs)

• 275.49 Other disorders of calcium metabolism (approximate)

Code annotations containing back-references to E20.1

Back-references to E20.1

• Type 1 Excludes: E31 Polyglandular dysfunction ("pseudohypoparathyroidism (E20.1)")
• Type 1 Excludes: E34 Other endocrine disorders ("pseudohypoparathyroidism (E20.1)")
• Type 2 Excludes: E34.8 Other specified endocrine disorders ("pseudohypoparathyroidism (E20.1)")

Back-references to E20

• Type 1 Excludes: E83 Disorders of mineral metabolism ("parathyroid disorders (E20-E21)")
• Code First: G63 Polyneuropathy in diseases classified elsewhere ("endocrine disease, except diabetes (E00-E07, E15-E16, E20-E34)")
• Code First: G73.7 Myopathy in diseases classified elsewhere ("hypoparathyroidism (E20.-)")
• Code First: H28 Cataract in diseases classified elsewhere ("hypoparathyroidism (E20.-)")

Diagnosis Index entries for E20.1

• Pseudohypoparathyroidism
• Pseudopseudohypoparathyroidism

Nearby codes

• E20 Hypoparathyroidism
• E20.0 Idiopathic hypoparathyroidism
• E20.1 Pseudohypoparathyroidism (this code)
• E20.8 Other hypoparathyroidism
• E20.81 Hypoparathyroidism due to impaired parathyroid hormone secretion
• E20.810 Autosomal dominant hypocalcemia
• E20.811 Secondary hypoparathyroidism in diseases classified elsewhere
• E20.812 Autoimmune hypoparathyroidism