G04.00 Acute disseminated encephalitis and encephalomyelitis, unspecified
Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.
Applies from G04 Encephalitis, myelitis and encephalomyelitis
Includes
- acute ascending myelitis
- meningoencephalitis
- meningomyelitis
Excludes1 (never code together)
- encephalopathy NOS (G93.40)
Excludes2 (not included here)
- acute transverse myelitis (G37.3)
- alcoholic encephalopathy (G31.2)
- multiple sclerosis (G35-)
- myalgic encephalomyelitis (G93.32)
- subacute necrotizing myelitis (G37.4)
- toxic encephalitis (G92.8)
- toxic encephalopathy (G92.8)
Applies from G04.0 Acute disseminated encephalitis and encephalomyelitis (ADEM)
Excludes1 (never code together)
- acute necrotizing hemorrhagic encephalopathy (G04.3-)
- other noninfectious acute disseminated encephalomyelitis (noninfectious ADEM) (G04.81)
MS-DRG index
Defines the logic of DRG(s) 023-024 in MDC 01.
Approximate ICD-9-CM (GEMs)
323.61 Infectious acute disseminated encephalomyelitis (ADEM) (approximate)
Code annotations containing back-references to G04.00
Back-references to G04.0
- Type 1 Excludes:
G04.3 Acute necrotizing hemorrhagic encephalopathy ("acute disseminated encephalitis and encephalomyelitis (G04.0-)")
Back-references to G04
- Type 1 Excludes:
G03 Meningitis due to other and unspecified causes ("meningoencephalitis (G04.-)") - Type 1 Excludes:
G03 Meningitis due to other and unspecified causes ("meningomyelitis (G04.-)") - Type 2 Excludes:
G95 Other and unspecified diseases of spinal cord ("myelitis (G04.-)")
Diagnosis Index entries for G04.00
- Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › acute › disseminated
- Encephalitis (chronic) (hemorrhagic) (idiopathic) (nonepidemic) (spurious) (subacute) › disseminated, acute
- Encephalomyelitis › acute disseminated
- Meningoencephalomyelitis › acute NEC (viral) › disseminated
Nearby codes
G04 Encephalitis, myelitis and encephalomyelitisG04.0 Acute disseminated encephalitis and encephalomyelitis (ADEM)G04.00 Acute disseminated encephalitis and encephalomyelitis, unspecified (this code)G04.01 Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)G04.02 Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitisG04.1 Tropical spastic paraplegiaG04.2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classifiedG04.3 Acute necrotizing hemorrhagic encephalopathy