G11.11 Friedreich ataxia

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Autosomal recessive Friedreich ataxia
• Friedreich ataxia with retained reflexes

Applies from G11 Hereditary ataxia

Excludes2 (not included here)

• cerebral palsy (G80.-)
• hereditary and idiopathic neuropathy (G60.-)
• metabolic disorders (E70-E88)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 200 — Friedreich and Other Hereditary Ataxias; Huntington Disease
• CMS-HCC V22: HCC 72 — Spinal Cord Disorders/Injuries
• ESRD V24: HCC 72

MS-DRG index

Defines the logic of DRG(s) 058-060 in MDC 01.

Code annotations containing back-references to G11.11

Back-references to G11

• Type 1 Excludes: R26 Abnormalities of gait and mobility ("hereditary ataxia (G11.-)")
• Type 1 Excludes: R27 Other lack of coordination ("hereditary ataxia (G11.-)")

Diagnosis Index entries for G11.11

• Ataxia, ataxy, ataxic › autosomal recessive Friedreich
• Ataxia, ataxy, ataxic › Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes)
• Ataxia, ataxy, ataxic › hereditary › spinal (Friedreich's)
• Ataxia, ataxy, ataxic › spinal › hereditary (Friedreich's)
• Cardiomyopathy (familial) (idiopathic) › due to › Friedreich's ataxia
• Disease, diseased › Friedreich's › combined systemic or ataxia
• Friedreich's › ataxia
• Friedreich's › combined systemic disease
• Friedreich's › sclerosis (cerebellum) (spinal cord)
• Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) › in (due to) › Friedreich's ataxia
• Sclerosis, sclerotic › Friedreich's (spinal cord)
• Sclerosis, sclerotic › hereditary › spinal (Friedreich's ataxia)
• Sclerosis, sclerotic › spinal (cord) (progressive) › hereditary (Friedreich's) (mixed form)

Nearby codes

• G11 Hereditary ataxia
• G11.0 Congenital nonprogressive ataxia
• G11.1 Early-onset cerebellar ataxia
• G11.10 Early-onset cerebellar ataxia, unspecified
• G11.11 Friedreich ataxia (this code)
• G11.19 Other early-onset cerebellar ataxia
• G11.2 Late-onset cerebellar ataxia
• G11.3 Cerebellar ataxia with defective DNA repair
• G11.4 Hereditary spastic paraplegia
• G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia