G12.1 Other inherited spinal muscular atrophy

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Adult form spinal muscular atrophy
• Childhood form, type II spinal muscular atrophy
• Distal spinal muscular atrophy
• Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander]
• Progressive bulbar palsy of childhood [Fazio-Londe]
• Scapuloperoneal form spinal muscular atrophy

Risk adjustment (HCC)

• CMS-HCC V28: HCC 190 — Amyotrophic Lateral Sclerosis and Other Motor Neuron Disease, Spinal Muscular Atrophy
• CMS-HCC V22: HCC 72 — Spinal Cord Disorders/Injuries
• RxHCC V08: HCC 155 — Spinal Cord Disorders
• ESRD V24: HCC 72

MS-DRG index

Defines the logic of DRG(s) 056-057 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 335.11 Kugelberg-Welander disease (approximate)

Diagnosis Index entries for G12.1

• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › progressive (bulbar) › adult
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › progressive (bulbar) › spinal › adult
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › adult form
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › childhood form, type II
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › distal
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › hereditary NEC
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › juvenile form, type III (Kugelberg- Welander)
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › scapuloperoneal form
• Fazio-Londe disease or syndrome
• Kugelberg-Welander disease
• Palsy › bulbar (progressive) (chronic) › of childhood (Fazio-Londe)

Nearby codes

• G12 Spinal muscular atrophy and related syndromes
• G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
• G12.1 Other inherited spinal muscular atrophy (this code)
• G12.2 Motor neuron disease
• G12.20 Motor neuron disease, unspecified
• G12.21 Amyotrophic lateral sclerosis
• G12.22 Progressive bulbar palsy
• G12.23 Primary lateral sclerosis