G71.11 Myotonic muscular dystrophy

Billable ICD-10-CM code, FY2026.

Applicable to

• Dystrophia myotonica [Steinert]
• Myotonia atrophica
• Myotonic dystrophy
• Proximal myotonic myopathy (PROMM)
• Steinert disease

Applies from G71 Primary disorders of muscles

Excludes2 (not included here)

• arthrogryposis multiplex congenita (Q74.3)
• metabolic disorders (E70-E88)
• myositis (M60.-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 197 — Muscular Dystrophy
• CMS-HCC V22: HCC 76 — Muscular Dystrophy
• ESRD V24: HCC 76

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 359.21 Myotonic muscular dystrophy

Code annotations containing back-references to G71.11

Back-references to G71.11

• Type 1 Excludes: E31 Polyglandular dysfunction ("dystrophia myotonica [Steinert] (G71.11)")

Back-references to G71.1

• Code First: H28 Cataract in diseases classified elsewhere ("myotonia (G71.1-)")

Back-references to G71

• Code First: M62.84 Sarcopenia ("primary disorders of muscles (G71.-)")

Diagnosis Index entries for G71.11

• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › myotonic
• Atrophy, atrophic (of) › myotonia
• Batten-Steinert syndrome
• Cardiomyopathy (familial) (idiopathic) › due to › myotonia atrophica
• Curschmann (-Batten) (-Steinert) disease or syndrome
• Disease, diseased › Batten-Steinert
• Disease, diseased › Curschmann
• Disease, diseased › Steinert's
• Dystrophy, dystrophia › muscular › congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) › myotonic
• Dystrophy, dystrophia › muscular › myotonic
• Dystrophy, dystrophia › myotonic, myotonica
• Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) › in (due to) › myotonia atrophica
• Myopathy › mytonic, proximal (PROMM)
• Myopathy › proximal myotonic (PROMM)
• Myotonia (acquisita) (intermittens) › atrophica
• Myotonia (acquisita) (intermittens) › dystrophica
• Steinert's disease
• Syndrome › Batten-Steinert
• Syndrome › Curschmann (-Batten) (-Steinert)

Nearby codes

• G71.036 Limb girdle muscular dystrophy due to fukutin related protein dysfunction
• G71.038 Other limb girdle muscular dystrophy
• G71.039 Limb girdle muscular dystrophy, unspecified
• G71.09 Other specified muscular dystrophies
• G71.1 Myotonic disorders
• G71.11 Myotonic muscular dystrophy (this code)
• G71.12 Myotonia congenita
• G71.13 Myotonic chondrodystrophy
• G71.14 Drug induced myotonia
• G71.19 Other specified myotonic disorders
• G71.2 Congenital myopathies