G71.220 X-linked myotubular myopathy

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Myotubular (centronuclear) myopathy

Applies from G71 Primary disorders of muscles

Excludes2 (not included here)

• arthrogryposis multiplex congenita (Q74.3)
• metabolic disorders (E70-E88)
• myositis (M60.-)

Applies from G71.2 Congenital myopathies

Excludes2 (not included here)

• arthrogryposis multiplex congenita (Q74.3)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 197 — Muscular Dystrophy
• CMS-HCC V22: HCC 76 — Muscular Dystrophy
• ESRD V24: HCC 76

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Code annotations containing back-references to G71.220

Back-references to G71

• Code First: M62.84 Sarcopenia ("primary disorders of muscles (G71.-)")

Diagnosis Index entries for G71.220

• Myopathy › myotubular (centronuclear)
• Myopathy › myotubular (centronuclear) › X-linked

Nearby codes

• G71.19 Other specified myotonic disorders
• G71.2 Congenital myopathies
• G71.20 Congenital myopathy, unspecified
• G71.21 Nemaline myopathy
• G71.22 Centronuclear myopathy
• G71.220 X-linked myotubular myopathy (this code)
• G71.228 Other centronuclear myopathy
• G71.29 Other congenital myopathy
• G71.3 Mitochondrial myopathy, not elsewhere classified
• G71.8 Other primary disorders of muscles
• G71.9 Primary disorder of muscle, unspecified