G90.B LMNB1-related autosomal dominant leukodystrophy

Billable ICD-10-CM code, FY2026.

Applies from G90 Disorders of autonomic nervous system

Excludes1 (never code together)

• dysfunction of the autonomic nervous system due to alcohol (G31.2)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 200 — Friedreich and Other Hereditary Ataxias; Huntington Disease
• ESRD V24: HCC 52

MS-DRG index

Defines the logic of DRG(s) 073-074 in MDC 01.

Diagnosis Index entries for G90.B

• Leukodystrophy › LMNB1-related autosomal dominant

Nearby codes

• G90.8 Other disorders of autonomic nervous system
• G90.81 Serotonin syndrome
• G90.89 Other disorders of autonomic nervous system
• G90.9 Disorder of the autonomic nervous system, unspecified
• G90.A Postural orthostatic tachycardia syndrome [POTS]
• G90.B LMNB1-related autosomal dominant leukodystrophy (this code)