G99.0 Autonomic neuropathy in diseases classified elsewhere

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Excludes1 (never code together)

• diabetic autonomic neuropathy (E08-E13 with .43)

Code first

• underlying disease, such as:
• amyloidosis (E85.-)
• gout (M1A.-, M10.-)
• hyperthyroidism (E05.-)

MS-DRG index

Defines the logic of DRG(s) 073-074 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 337.1 Peripheral autonomic neuropathy in disorders classified elsewhere

Medicare Code Edits (MCE v43.1 (April 2026))

• Manifestation codes as principal diagnosis: Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and are not allowed as principal diagnosis.

Code annotations containing back-references to G99.0

Back-references to G99.0

• Use Additional: M1A Chronic gout ("Autonomic neuropathy in diseases classified elsewhere (G99.0)")
• Use Additional: M10 Gout ("Autonomic neuropathy in diseases classified elsewhere (G99.0)")

Diagnosis Index entries for G99.0

• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › amyloidosis
• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › endocrine disease NEC
• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › gout
• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › hyperthyroidism
• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › hyperthyroidism › with thyroid storm
• Neuropathy, neuropathic › peripheral (nerve) › autonomic › in (due to) › metabolic disease NEC

Nearby codes

• G99 Other disorders of nervous system in diseases classified elsewhere
• G99.0 Autonomic neuropathy in diseases classified elsewhere (this code)
• G99.2 Myelopathy in diseases classified elsewhere
• G99.8 Other specified disorders of nervous system in diseases classified elsewhere