H31.21 Choroideremia

Billable ICD-10-CM code, FY2026.

Applies from H31.2 Hereditary choroidal dystrophy

Excludes2 (not included here)

• hyperornithinemia (E72.4)
• ornithinemia (E72.4)

MS-DRG index

Defines the logic of DRG(s) 124-125 in MDC 02.

Approximate ICD-9-CM (GEMs)

• 363.55 Choroideremia

Code annotations containing back-references to H31.21

Back-references to H31.2

• Type 1 Excludes: E72.4 Disorders of ornithine metabolism ("hereditary choroidal dystrophy (H31.2-)")

Back-references to H31

• Use Additional: H44.2A Degenerative myopia with choroidal neovascularization ("code for any associated choroid disorders (H31.-)")

Diagnosis Index entries for H31.21

• Choroideremia
• Dystrophy, dystrophia › choroid (hereditary) › choroideremia

Nearby codes

• H31.122 Diffuse secondary atrophy of choroid, left eye
• H31.123 Diffuse secondary atrophy of choroid, bilateral
• H31.129 Diffuse secondary atrophy of choroid, unspecified eye
• H31.2 Hereditary choroidal dystrophy
• H31.20 Hereditary choroidal dystrophy, unspecified
• H31.21 Choroideremia (this code)
• H31.22 Choroidal dystrophy (central areolar) (generalized) (peripapillary)
• H31.23 Gyrate atrophy, choroid
• H31.29 Other hereditary choroidal dystrophy
• H31.3 Choroidal hemorrhage and rupture
• H31.30 Unspecified choroidal hemorrhage