H35.54 Dystrophies primarily involving the retinal pigment epithelium

Billable ICD-10-CM code, FY2026.

Applicable to

• Vitelliform retinal dystrophy

Applies from H35 Other retinal disorders

Excludes2 (not included here)

• diabetic retinal disorders (E08.311-E08.359, E09.311-E09.359, E10.311-E10.359, E11.311-E11.359, E13.311-E13.359)

Applies from H35.5 Hereditary retinal dystrophy

Excludes1 (never code together)

• dystrophies primarily involving Bruch's membrane (H31.1-)

MS-DRG index

Defines the logic of DRG(s) 124-125 in MDC 02.

Approximate ICD-9-CM (GEMs)

• 362.76 Dystrophies primarily involving the retinal pigment epithelium

Code annotations containing back-references to H35.54

Back-references to H35.5

• Type 1 Excludes: H35.4 Peripheral retinal degeneration ("hereditary retinal degeneration (dystrophy) (H35.5-)")

Diagnosis Index entries for H35.54

• Dystrophy, dystrophia › retinal (hereditary) › involving › pigment epithelium
• Dystrophy, dystrophia › tapetoretinal

Nearby codes

• H35.5 Hereditary retinal dystrophy
• H35.50 Unspecified hereditary retinal dystrophy
• H35.51 Vitreoretinal dystrophy
• H35.52 Pigmentary retinal dystrophy
• H35.53 Other dystrophies primarily involving the sensory retina
• H35.54 Dystrophies primarily involving the retinal pigment epithelium (this code)
• H35.6 Retinal hemorrhage
• H35.60 Retinal hemorrhage, unspecified eye
• H35.61 Retinal hemorrhage, right eye
• H35.62 Retinal hemorrhage, left eye
• H35.63 Retinal hemorrhage, bilateral