H36.89 Other retinal disorders in diseases classified elsewhere

Billable ICD-10-CM code, FY2026.

Applicable to

• Retinal dystrophy in lipid storage disorders

Applies from H36 Retinal disorders in diseases classified elsewhere

Excludes1 (never code together)

• arteriosclerotic retinopathy (H35.0-)
• diabetic retinopathy (E08.3-, E09.3-, E10.3-, E11.3-, E13.3-)

Code first

• underlying disease, such as:
• lipid storage disorders (E75.-)
• sickle-cell disorders (D57.-)

MS-DRG index

Defines the logic of DRG(s) 124-125 in MDC 02.

Medicare Code Edits (MCE v43.1 (April 2026))

• Manifestation codes as principal diagnosis: Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and are not allowed as principal diagnosis.

Diagnosis Index entries for H36.89

• Batten (-Mayou) disease › retina
• Disease, diseased › retina, retinal › Batten's or Batten-Mayou
• Dystrophy, dystrophia › retinal (hereditary) › in › lipid storage disorders
• Dystrophy, dystrophia › retinal (hereditary) › in › systemic lipidoses

Nearby codes

• H36.82 Proliferative sickle-cell retinopathy
• H36.821 Proliferative sickle-cell retinopathy, right eye
• H36.822 Proliferative sickle-cell retinopathy, left eye
• H36.823 Proliferative sickle-cell retinopathy, bilateral
• H36.829 Proliferative sickle-cell retinopathy, unspecified eye
• H36.89 Other retinal disorders in diseases classified elsewhere (this code)