I27.29 Other secondary pulmonary hypertension

Billable ICD-10-CM code, FY2026.

Applicable to

• Group 5 pulmonary hypertension
• Pulmonary hypertension with unclear multifactorial mechanisms
• Pulmonary hypertension due to hematologic disorders
• Pulmonary hypertension due to metabolic disorders
• Pulmonary hypertension due to other systemic disorders

Code also

• other associated disorders, if known, such as:
• chronic myeloid leukemia (C92.10-C92.22)
• essential thrombocythemia (D47.3)
• Gaucher disease (E75.22)
• hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
• hyperthyroidism (E05.-)
• hypothyroidism (E00-E03)
• polycythemia vera (D45)
• sarcoidosis (D86.-)

Applies from I27.2 Other secondary pulmonary hypertension

Excludes1 (never code together)

• Eisenmenger's syndrome (I27.83)

Code also

• associated underlying condition

Risk adjustment (HCC)

• CMS-HCC V28: HCC 226 — Heart Failure, Except End-Stage and Acute
• CMS-HCC V22: HCC 85 — Congestive Heart Failure
• RxHCC V08: HCC 184 — Pulmonary Hypertension, Except Arterial, and Other Pulmonary Heart Disease
• ESRD V24: HCC 85

MS-DRG index

Defines the logic of DRG(s) 314-316 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 416.8 Other chronic pulmonary heart diseases (approximate)

Code annotations containing back-references to I27.29

Back-references to I27.29

• Type 1 Excludes: I27.0 Primary pulmonary hypertension ("secondary pulmonary hypertension (I27.29)")

Back-references to I27.2

• Code First: I5A Non-ischemic myocardial injury (non-traumatic) ("pulmonary hypertension (I27.0, I27.2-)")
• Use Additional: P24.01 Meconium aspiration with respiratory symptoms ("code to identify any secondary pulmonary hypertension, if applicable (I27.2-)")
• Use Additional: P24.11 Neonatal aspiration of (clear) amniotic fluid and mucus with respiratory symptoms ("code to identify any secondary pulmonary hypertension, if applicable (I27.2-)")
• Use Additional: P24.21 Neonatal aspiration of blood with respiratory symptoms ("code to identify any secondary pulmonary hypertension, if applicable (I27.2-)")
• Use Additional: P24.31 Neonatal aspiration of milk and regurgitated food with respiratory symptoms ("code to identify any secondary pulmonary hypertension, if applicable (I27.2-)")
• Use Additional: P24.81 Other neonatal aspiration with respiratory symptoms ("code to identify any secondary pulmonary hypertension, if applicable (I27.2-)")

Diagnosis Index entries for I27.29

• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › with › cor pulmonale (chronic)
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › with › right heart ventricular strain/failure
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › with › unclear multifactorial mechanisms
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › due to › hematologic disorders
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › due to › metabolic disorders
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › due to › specified systemic disorders NEC
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › group 5
• Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › secondary › specified NEC

Nearby codes

• I27.20 Pulmonary hypertension, unspecified
• I27.21 Secondary pulmonary arterial hypertension
• I27.22 Pulmonary hypertension due to left heart disease
• I27.23 Pulmonary hypertension due to lung diseases and hypoxia
• I27.24 Chronic thromboembolic pulmonary hypertension
• I27.29 Other secondary pulmonary hypertension (this code)
• I27.8 Other specified pulmonary heart diseases
• I27.81 Cor pulmonale (chronic)
• I27.82 Chronic pulmonary embolism
• I27.83 Eisenmenger's syndrome
• I27.84 Fontan related circulation