I27.841 Fontan-associated lymphatic dysfunction

Billable ICD-10-CM code, FY2026.

Code also

• associated conditions such as:
• chylothorax (J94.0)
• Fontan associated protein-losing enteropathy (K90.89)
• plastic (obstructive) bronchitis (J44.89)

Risk adjustment (HCC)

• RxHCC V08: HCC 191 — Ventricular Septal Defect and Major Congenital Heart Disorders

MS-DRG index

Defines the logic of DRG(s) 808-810 in MDC 16.

Code annotations containing back-references to I27.841

Back-references to I27.84

• Type 2 Excludes: Z98 Other postprocedural states ("Fontan related circulation (I27.84-)")

Diagnosis Index entries for I27.841

• Circulation › Fontan related › with › Fontan-associated lymphatic dysfunction
• Dysfunction › lymphatic › Fontan-associated

Nearby codes

• I27.81 Cor pulmonale (chronic)
• I27.82 Chronic pulmonary embolism
• I27.83 Eisenmenger's syndrome
• I27.84 Fontan related circulation
• I27.840 Fontan-associated liver disease [FALD]
• I27.841 Fontan-associated lymphatic dysfunction (this code)
• I27.848 Other Fontan-associated condition
• I27.849 Fontan related circulation, unspecified
• I27.89 Other specified pulmonary heart diseases
• I27.9 Pulmonary heart disease, unspecified