I28.0 Arteriovenous fistula of pulmonary vessels

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Excludes1 (never code together)

• congenital arteriovenous fistula (Q25.72)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 226 — Heart Failure, Except End-Stage and Acute
• CMS-HCC V22: HCC 85 — Congestive Heart Failure
• RxHCC V08: HCC 184 — Pulmonary Hypertension, Except Arterial, and Other Pulmonary Heart Disease
• ESRD V24: HCC 85

MS-DRG index

Defines the logic of DRG(s) 314-316 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 417.0 Arteriovenous fistula of pulmonary vessels

Code annotations containing back-references to I28.0

Back-references to I28

• Type 2 Excludes: I77 Other disorders of arteries and arterioles ("pulmonary artery (I28.-)")

Diagnosis Index entries for I28.0

• Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) › arteriovenous (congenital) › acquired › pulmonary
• Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) › pulmonary › arteriovenous › acquired
• Fistula (cutaneous) › arteriovenous (acquired) (nonruptured) › pulmonary
• Fistula (cutaneous) › pulmonary › arteriovenous
• Shunt › arteriovenous, pulmonary (acquired)

Nearby codes

• I28 Other diseases of pulmonary vessels
• I28.0 Arteriovenous fistula of pulmonary vessels (this code)
• I28.1 Aneurysm of pulmonary artery
• I28.8 Other diseases of pulmonary vessels
• I28.9 Disease of pulmonary vessels, unspecified