I40.1 Isolated myocarditis
Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.
Applicable to
- Fiedler's myocarditis
- Giant cell myocarditis
- Idiopathic myocarditis
Applies from I40 Acute myocarditis
Includes
Excludes1 (never code together)
- acute rheumatic myocarditis (I01.2)
MS-DRG index
Defines the logic of DRG(s) 314-316 in MDC 05.
Approximate ICD-9-CM (GEMs)
422.91 Idiopathic myocarditis (approximate)
Code annotations containing back-references to I40.1
Back-references to I40
- Type 1 Excludes:
I51.4 Myocarditis, unspecified ("acute or subacute myocarditis (I40.-)") - Code First:
I5A Non-ischemic myocardial injury (non-traumatic) ("acute myocarditis (I40.-)") - Code Also:
M35.81 Multisystem inflammatory syndrome ("acute myocarditis (I40.-)")
Diagnosis Index entries for I40.1
- Abramov-Fiedler myocarditis (acute isolated myocarditis)
- Fiedler's › myocarditis (acute)
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › acute or subacute (interstitial) › idiopathic
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › eosinophilic
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › Fiedler's (acute) (isolated)
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › giant cell (acute) (subacute)
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › granulomatous (idiopathic) (isolated) (nonspecific)
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › idiopathic (granulomatous)
- Myocarditis (with arteriosclerosis)(chronic)(fibroid) (interstitial) (old) (progressive) (senile) › isolated (acute)
- Syndrome › Fiedler's
Nearby codes
I40 Acute myocarditisI40.0 Infective myocarditisI40.1 Isolated myocarditis (this code)I40.8 Other acute myocarditisI40.9 Acute myocarditis, unspecified