I78.0 Hereditary hemorrhagic telangiectasia
Billable ICD-10-CM code, FY2026.
Applicable to
- Rendu-Osler-Weber disease
Risk adjustment (HCC)
- CMS-HCC V22: HCC 108 — Vascular Disease
- ESRD V24: HCC 108
MS-DRG index
Defines the logic of DRG(s) 299-301 in MDC 05.
Approximate ICD-9-CM (GEMs)
448.0 Hereditary hemorrhagic telangiectasia
Diagnosis Index entries for I78.0
- Angioma › hemorrhagicum hereditaria
- Angiomatosis › hemorrhagic familial
- Angiomatosis › hereditary familial
- Babington's disease (familial hemorrhagic telangiectasia)
- Disease, diseased › Babington's (familial hemorrhagic telangiectasia)
- Disease, diseased › Goldstein's (familial hemorrhagic telangiectasia)
- Disease, diseased › Osler-Rendu (familial hemorrhagic telangiectasia)
- Disease, diseased › Rendu-Osler-Weber (familial hemorrhagic telangiectasia)
- Epistaxis (multiple) › hereditary
- Goldstein's disease (familial hemorrhagic telangiectasia)
- Osler (-Weber)-Rendu disease
- Rendu-Osler-Weber disease or syndrome
- Syndrome › Osler-Weber-Rendu
- Syndrome › Rendu-Osler-Weber
- Telangiectasia, telangiectasis (verrucous) › familial
- Telangiectasia, telangiectasis (verrucous) › hemorrhagic, hereditary (congenital) (senile)
- Telangiectasia, telangiectasis (verrucous) › hereditary, hemorrhagic (congenital) (senile)
- Weber-Osler syndrome
Nearby codes
I78 Diseases of capillariesI78.0 Hereditary hemorrhagic telangiectasia (this code)I78.1 Nevus, non-neoplasticI78.8 Other diseases of capillariesI78.9 Disease of capillaries, unspecified