I89.0 Lymphedema, not elsewhere classified

Billable ICD-10-CM code, FY2026.

Applicable to

• Elephantiasis (nonfilarial) NOS
• Lymphangiectasis
• Obliteration, lymphatic vessel
• Praecox lymphedema
• Secondary lymphedema

Excludes1 (never code together)

• postmastectomy lymphedema (I97.2)

Applies from I89 Other noninfective disorders of lymphatic vessels and lymph nodes

Excludes1 (never code together)

• chylocele, tunica vaginalis (nonfilarial) NOS (N50.89)
• enlarged lymph nodes NOS (R59.-)
• filarial chylocele (B74.-)
• hereditary lymphedema (Q82.0)

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 457.1 Other lymphedema

Code annotations containing back-references to I89.0

Back-references to I89.0

• Use Additional: Q93.52 Phelan-McDermid syndrome ("lymphedema (I89.0)")

Diagnosis Index entries for I89.0

• Compression › lymphatic vessel
• Dilatation › lymphatic vessel
• Edema, edematous (infectious) (pitting) (toxic) › due to › lymphatic obstruction
• Edema, edematous (infectious) (pitting) (toxic) › lymphatic
• Elephantiasis (nonfilarial)
• Elephantiasis (nonfilarial) › glandular
• Elephantiasis (nonfilarial) › lymphangiectatic
• Elephantiasis (nonfilarial) › lymphatic vessel
• Elephantiasis (nonfilarial) › scrotum (nonfilarial)
• Elephantiasis (nonfilarial) › streptococcal
• Elephantiasis (nonfilarial) › telangiectodes
• Lymphangiectasis
• Lymphangiectasis › postinfectional
• Lymphangiectasis › scrotum
• Lymphangiectatic elephantiasis, nonfilarial
• Lymphectasia
• Lymphedema (acquired) › praecox
• Lymphedema (acquired) › secondary
• Obliteration › lymphatic vessel
• Obstruction, obstructed, obstructive › lymphatic
• Obstruction, obstructed, obstructive › thoracic duct
• Occlusion, occluded › lymph or lymphatic channel
• Occlusion, occluded › thoracic duct

Nearby codes

• I89 Other noninfective disorders of lymphatic vessels and lymph nodes
• I89.0 Lymphedema, not elsewhere classified (this code)
• I89.1 Lymphangitis
• I89.8 Other specified noninfective disorders of lymphatic vessels and lymph nodes
• I89.9 Noninfective disorder of lymphatic vessels and lymph nodes, unspecified