J43.0 Unilateral pulmonary emphysema [MacLeod's syndrome]

Billable ICD-10-CM code, FY2026.

Applicable to

• Swyer-James syndrome
• Unilateral emphysema
• Unilateral hyperlucent lung
• Unilateral pulmonary artery functional hypoplasia
• Unilateral transparency of lung

Applies from J43 Emphysema

Excludes1 (never code together)

• compensatory emphysema (J98.3)
• interstitial emphysema (J98.2)
• mediastinal emphysema (J98.2)
• neonatal interstitial emphysema (P25.0)
• surgical (subcutaneous) emphysema (T81.82)

Excludes2 (not included here)

• emphysema due to inhalation of chemicals, gases, fumes or vapors (J68.4)
• emphysema with chronic (obstructive) bronchitis (J44.-)
• emphysematous (obstructive) bronchitis (J44.-)
• traumatic subcutaneous emphysema (T79.7)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders
• CMS-HCC V22: HCC 111 — Chronic Obstructive Pulmonary Disease
• RxHCC V08: HCC 229 — Chronic Obstructive Pulmonary Disease, Bronchiectasis, and Other Asthma
• ESRD V24: HCC 111

MS-DRG index

Defines the logic of DRG(s) 190-192 in MDC 04.

Approximate ICD-9-CM (GEMs)

• 492.8 Other emphysema (approximate)

Code annotations containing back-references to J43.0

Back-references to J43

• Type 2 Excludes: J44 Other chronic obstructive pulmonary disease ("emphysema without chronic bronchitis (J43.-)")
• Code Also: J68.4 Chronic respiratory conditions due to chemicals, gases, fumes and vapors ("emphysema (J43.-)")
• Type 2 Excludes: T79.7 Traumatic subcutaneous emphysema ("emphysema NOS (J43)")

Diagnosis Index entries for J43.0

• Emphysema (atrophic) (bullous) (chronic) (interlobular) (lung) (obstructive) (pulmonary) (senile) (vesicular) › unilateral
• Hyperlucent lung, unilateral
• Hypoplasia, hypoplastic › artery (peripheral) › pulmonary › functional, unilateral
• Hypoplasia, hypoplastic › pulmonary (not associated with short gestation) › artery, functional
• MacLeod's syndrome
• Transparency, lung, unilateral

Nearby codes

• J43 Emphysema
• J43.0 Unilateral pulmonary emphysema [MacLeod's syndrome] (this code)
• J43.1 Panlobular emphysema
• J43.2 Centrilobular emphysema
• J43.8 Other emphysema
• J43.9 Emphysema, unspecified