J84.01 Alveolar proteinosis

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applies from J84 Other interstitial pulmonary diseases

Excludes1 (never code together)

• drug-induced interstitial lung disorders (J70.2-J70.4)
• interstitial emphysema (J98.2)

Excludes2 (not included here)

• lung diseases due to external agents (J60-J70)

Code also

• , if applicable, associated condition

Risk adjustment (HCC)

• CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders
• CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
• RxHCC V08: HCC 227 — Pulmonary Fibrosis, Except Idiopathic
• ESRD V24: HCC 112

MS-DRG index

Defines the logic of DRG(s) 196-198 in MDC 04.

Approximate ICD-9-CM (GEMs)

• 516.0 Pulmonary alveolar proteinosis

Code annotations containing back-references to J84.01

Back-references to J84

• Code Also: I27.23 Pulmonary hypertension due to lung diseases and hypoxia ("interstitial lung disease (J84.-)")

Diagnosis Index entries for J84.01

• Proteinosis › alveolar (pulmonary)

Nearby codes

• J84 Other interstitial pulmonary diseases
• J84.0 Alveolar and parieto-alveolar conditions
• J84.01 Alveolar proteinosis (this code)
• J84.02 Pulmonary alveolar microlithiasis
• J84.03 Idiopathic pulmonary hemosiderosis
• J84.09 Other alveolar and parieto-alveolar conditions
• J84.1 Other interstitial pulmonary diseases with fibrosis
• J84.10 Pulmonary fibrosis, unspecified