J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Billable ICD-10-CM code, FY2026.

Applicable to

• Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
• Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
• Organizing pneumonia due to collagen vascular disease
• Organizing pneumonia in diseases classified elsewhere

Code first

• underlying disease, such as:
• progressive systemic sclerosis (M34.0)
• rheumatoid arthritis (M05.00-M06.9)
• systemic lupus erythematosis (M32.0-M32.9)

Applies from J84 Other interstitial pulmonary diseases

Excludes1 (never code together)

• drug-induced interstitial lung disorders (J70.2-J70.4)
• interstitial emphysema (J98.2)

Excludes2 (not included here)

• lung diseases due to external agents (J60-J70)

Code also

• , if applicable, associated condition

Applies from J84.1 Other interstitial pulmonary diseases with fibrosis

Excludes1 (never code together)

• pulmonary fibrosis (chronic) following radiation (J70.1)

Code also

• , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 280 — Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders
• CMS-HCC V22: HCC 112 — Fibrosis of Lung and Other Chronic Lung Disorders
• RxHCC V08: HCC 227 — Pulmonary Fibrosis, Except Idiopathic
• ESRD V24: HCC 112

MS-DRG index

Defines the logic of DRG(s) 196-198 in MDC 04.

Medicare Code Edits (MCE v43.1 (April 2026))

• Manifestation codes as principal diagnosis: Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and are not allowed as principal diagnosis.

Code annotations containing back-references to J84.178

Back-references to J84.178

• Type 1 Excludes: J18 Pneumonia, unspecified organism ("usual interstitial pneumonia (J84.178)")

Back-references to J84

• Code Also: I27.23 Pulmonary hypertension due to lung diseases and hypoxia ("interstitial lung disease (J84.-)")

Diagnosis Index entries for J84.178

• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › due to › collagen vascular disease
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › due to › known underlying cause
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › in disease classified elsewhere
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › lymphocytic (due to collagen vascular disease) (in diseases classified elsewhere)
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › non-specific › due to › collagen vascular disease
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › non-specific › due to › known underlying cause
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › non-specific › in diseases classified elsewhere
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › usual › due to collagen vascular disease
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › interstitial › usual › in diseases classified elsewhere
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › organizing › due to › collagen vascular disease
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › organizing › due to › known underlying cause
• Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) › organizing › in diseases classified elsewhere

Nearby codes

• J84.115 Respiratory bronchiolitis interstitial lung disease
• J84.116 Cryptogenic organizing pneumonia
• J84.117 Desquamative interstitial pneumonia
• J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
• J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
• J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere (this code)
• J84.2 Lymphoid interstitial pneumonia
• J84.8 Other specified interstitial pulmonary diseases
• J84.81 Lymphangioleiomyomatosis
• J84.82 Adult pulmonary Langerhans cell histiocytosis
• J84.83 Surfactant mutations of the lung