K00.5 Hereditary disturbances in tooth structure, not elsewhere classified

Billable ICD-10-CM code, FY2026.

Applicable to

• Amelogenesis imperfecta
• Dentinogenesis imperfecta
• Odontogenesis imperfecta
• Dentinal dysplasia
• Shell teeth

Applies from K00 Disorders of tooth development and eruption

Excludes2 (not included here)

• embedded and impacted teeth (K01.-)

MS-DRG index

Defines the logic of DRG(s) 011-013 in MDC PRE.

Approximate ICD-9-CM (GEMs)

• 520.5 Hereditary disturbances in tooth structure, not elsewhere classified

Diagnosis Index entries for K00.5

• Amelogenesis imperfecta
• Brown enamel of teeth (hereditary)
• Defect, defective › dentin (hereditary)
• Dentin › opalescent
• Dentinogenesis imperfecta
• Disturbance (s) › tooth › structure, hereditary NEC
• Dysplasia › dentinal
• Odontogenesis imperfecta
• Opalescent dentin (hereditary)
• Shell teeth

Nearby codes

• K00.0 Anodontia
• K00.1 Supernumerary teeth
• K00.2 Abnormalities of size and form of teeth
• K00.3 Mottled teeth
• K00.4 Disturbances in tooth formation
• K00.5 Hereditary disturbances in tooth structure, not elsewhere classified (this code)
• K00.6 Disturbances in tooth eruption
• K00.7 Teething syndrome
• K00.8 Other disorders of tooth development
• K00.9 Disorder of tooth development, unspecified