K74.3 Primary biliary cirrhosis

Billable ICD-10-CM code, FY2026.

Applicable to

• Chronic nonsuppurative destructive cholangitis
• Primary biliary cholangitis

Excludes2 (not included here)

• primary sclerosing cholangitis (K83.01)

Applies from K74 Fibrosis and cirrhosis of liver

Excludes1 (never code together)

• alcoholic cirrhosis (of liver) (K70.3)
• alcoholic fibrosis of liver (K70.2)
• cardiac sclerosis of liver (K76.1)
• cirrhosis (of liver) with toxic liver disease (K71.7)
• congenital cirrhosis (of liver) (P78.81)
• pigmentary cirrhosis (of liver) (E83.110)

Code also

• , if applicable, viral hepatitis (acute) (chronic) (B15-B19)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 68 — Cholangitis and Obstruction of Bile Duct Without Gallstones
• CMS-HCC V22: HCC 28 — Cirrhosis of Liver
• RxHCC V08: HCC 59 — Primary Biliary Cirrhosis
• ESRD V24: HCC 28

MS-DRG index

Defines the logic of DRG(s) 432-434 in MDC 07.

Approximate ICD-9-CM (GEMs)

• 571.6 Biliary cirrhosis (approximate)

Code annotations containing back-references to K74.3

Back-references to K74.3

• Type 2 Excludes: K83.0 Cholangitis ("chronic nonsuppurative destructive cholangitis (K74.3)")
• Type 2 Excludes: K83.0 Cholangitis ("primary biliary cholangitis (K74.3)")
• Type 2 Excludes: K83.0 Cholangitis ("primary biliary cirrhosis (K74.3)")

Diagnosis Index entries for K74.3

• Charcot's › cirrhosis
• Cholangitis (ascending) (recurrent) (secondary) (stenosing) (suppurative) › chronic nonsuppurative destructive
• Cirrhosis, cirrhotic (hepatic) (liver) › biliary (cholangiolitic) (cholangitic) (hypertrophic) (obstructive) (pericholangiolitic) › primary
• Cirrhosis, cirrhotic (hepatic) (liver) › Charcot's
• Cirrhosis, cirrhotic (hepatic) (liver) › cholangiolitic, cholangitic, cholostatic (primary)
• Cirrhosis, cirrhotic (hepatic) (liver) › Hanot's (hypertrophic)
• Cirrhosis, cirrhotic (hepatic) (liver) › hypertrophic
• Cirrhosis, cirrhotic (hepatic) (liver) › monolobular
• Cirrhosis, cirrhotic (hepatic) (liver) › Todd's
• Cirrhosis, cirrhotic (hepatic) (liver) › unilobar
• Hanot's cirrhosis or disease
• Todd's › cirrhosis

Nearby codes

• K74.00 Hepatic fibrosis, unspecified
• K74.01 Hepatic fibrosis, early fibrosis
• K74.02 Hepatic fibrosis, advanced fibrosis
• K74.1 Hepatic sclerosis
• K74.2 Hepatic fibrosis with hepatic sclerosis
• K74.3 Primary biliary cirrhosis (this code)
• K74.4 Secondary biliary cirrhosis
• K74.5 Biliary cirrhosis, unspecified
• K74.6 Other and unspecified cirrhosis of liver
• K74.60 Unspecified cirrhosis of liver
• K74.69 Other cirrhosis of liver