L10.81 Paraneoplastic pemphigus

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applies from L10 Pemphigus

Excludes1 (never code together)

• pemphigus neonatorum (L01.03)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 387 — Pemphigus, Pemphigoid, and Other Specified Autoimmune Skin Disorders
• RxHCC V08: HCC 314 — Pemphigus, Pemphigoid, and Other Bullous Skin Disorders

MS-DRG index

Defines the logic of DRG(s) 595-596 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 694.4 Pemphigus (approximate)

Diagnosis Index entries for L10.81

• Pemphigus › paraneoplastic

Nearby codes

• L10.2 Pemphigus foliaceous
• L10.3 Brazilian pemphigus [fogo selvagem]
• L10.4 Pemphigus erythematosus
• L10.5 Drug-induced pemphigus
• L10.8 Other pemphigus
• L10.81 Paraneoplastic pemphigus (this code)
• L10.89 Other pemphigus
• L10.9 Pemphigus, unspecified