L81.3 Café au lait spots

Billable ICD-10-CM code, FY2026.

Applies from L81 Other disorders of pigmentation

Excludes1 (never code together)

• birthmark NOS (Q82.5)
• Peutz-Jeghers syndrome (Q85.89)

Excludes2 (not included here)

• nevus - see Alphabetical Index

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 709.09 Other dyschromia (approximate)

Code annotations containing back-references to L81.3

Back-references to L81.3

• Type 2 Excludes: Q82.5 Congenital non-neoplastic nevus ("Café au lait spots (L81.3)")

Diagnosis Index entries for L81.3

• Café, au lait spots
• Spots, spotting (in) (of) › café, au lait

Nearby codes

• L81 Other disorders of pigmentation
• L81.0 Postinflammatory hyperpigmentation
• L81.1 Chloasma
• L81.2 Freckles
• L81.3 Cafe au lait spots (this code)
• L81.4 Other melanin hyperpigmentation
• L81.5 Leukoderma, not elsewhere classified
• L81.6 Other disorders of diminished melanin formation
• L81.7 Pigmented purpuric dermatosis
• L81.8 Other specified disorders of pigmentation