L94.1 Linear scleroderma

Billable ICD-10-CM code, FY2026.

Applicable to

• En coup de sabre lesion

Applies from L94 Other localized connective tissue disorders

Excludes1 (never code together)

• systemic connective tissue disorders (M30-M36)

MS-DRG index

Defines the logic of DRG(s) 606-607 in MDC 09.

Approximate ICD-9-CM (GEMs)

• 701.0 Circumscribed scleroderma (approximate)

Diagnosis Index entries for L94.1

• En coup de sabre lesion
• Lesion (s) (nontraumatic) › en coup de sabre
• Scleroderma, sclerodermia (acrosclerotic) (diffuse) (generalized) (progressive) (pulmonary) › linear

Nearby codes

• L94 Other localized connective tissue disorders
• L94.0 Localized scleroderma [morphea]
• L94.1 Linear scleroderma (this code)
• L94.2 Calcinosis cutis
• L94.3 Sclerodactyly
• L94.4 Gottron's papules
• L94.5 Poikiloderma vasculare atrophicans
• L94.6 Ainhum