M35.9 Systemic involvement of connective tissue, unspecified
Billable ICD-10-CM code, FY2026.
Applicable to
- Autoimmune disease (systemic) NOS
- Collagen (vascular) disease NOS
Applies from M35 Other systemic involvement of connective tissue
Excludes1 (never code together)
- reactive perforating collagenosis (L87.1)
Risk adjustment (HCC)
- CMS-HCC V22: HCC 40 — Rheumatoid Arthritis and Inflammatory Connective Tissue Disease
- RxHCC V08: HCC 84 — Systemic Lupus Erythematosus and Other Systemic Connective Tissue Disorders
- ESRD V24: HCC 40
MS-DRG index
Defines the logic of DRG(s) 545-547 in MDC 08.
Approximate ICD-9-CM (GEMs)
710.9 Unspecified diffuse connective tissue disease (approximate)
Code annotations containing back-references to M35.9
Back-references to M35.9
- Code First:
G32.81 Cerebellar ataxia in diseases classified elsewhere ("non-celiac gluten ataxia (M35.9)")
Back-references to M35
- Type 2 Excludes:
I77 Other disorders of arteries and arterioles ("collagen (vascular) diseases (M30-M36)") - Type 2 Excludes:
J82 Pulmonary eosinophilia, not elsewhere classified ("pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)") - Code First:
J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere ("systemic connective tissue disorders (M30-M36)") - Type 1 Excludes:
L94 Other localized connective tissue disorders ("systemic connective tissue disorders (M30-M36)")
Diagnosis Index entries for M35.9
- Ataxia, ataxy, ataxic › gluten
- Autoimmune › disease (systemic)
- Collagenosis, collagen disease (nonvascular) (vascular)
- Disease, diseased › autoimmune (systemic) NOS
- Disease, diseased › collagen NOS (nonvascular) (vascular)
- Disease, diseased › connective tissue, systemic (diffuse)
- Disease, diseased › mesenchymal
- Dyscollagenosis
- Polyneuropathy (peripheral) › in (due to) › collagen vascular disease NEC
- Polyneuropathy (peripheral) › in (due to) › systemic › connective tissue disorder
- Skin › hidebound
- Syndrome › connective tissue
Nearby codes
M35.6 Relapsing panniculitis [Weber-Christian]M35.7 Hypermobility syndromeM35.8 Other specified systemic involvement of connective tissueM35.81 Multisystem inflammatory syndromeM35.89 Other specified systemic involvement of connective tissueM35.9 Systemic involvement of connective tissue, unspecified (this code)