N00.1 Acute nephritic syndrome with focal and segmental glomerular lesions

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.

Applicable to

• Acute nephritic syndrome with focal and segmental hyalinosis
• Acute nephritic syndrome with focal and segmental sclerosis
• Acute nephritic syndrome with focal glomerulonephritis

Applies from N00 Acute nephritic syndrome

Includes

• acute glomerular disease
• acute glomerulonephritis
• acute nephritis

Excludes1 (never code together)

• acute tubulo-interstitial nephritis (N10)
• nephritic syndrome NOS (N05.-)

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 580.0 Acute glomerulonephritis with lesion of proliferative glomerulonephritis (approximate)

Diagnosis Index entries for N00.1

• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › acute › with › focal and segmental glomerular lesions

Nearby codes

• N00 Acute nephritic syndrome
• N00.0 Acute nephritic syndrome with minor glomerular abnormality
• N00.1 Acute nephritic syndrome with focal and segmental glomerular lesions (this code)
• N00.2 Acute nephritic syndrome with diffuse membranous glomerulonephritis
• N00.3 Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
• N00.4 Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
• N00.5 Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
• N00.6 Acute nephritic syndrome with dense deposit disease