N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis.

Applicable to

• Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
• Rapidly progressive nephritic syndrome with focal and segmental sclerosis
• Rapidly progressive nephritic syndrome with focal glomerulonephritis

Applies from N01 Rapidly progressive nephritic syndrome

Includes

• rapidly progressive glomerular disease
• rapidly progressive glomerulonephritis
• rapidly progressive nephritis

Excludes1 (never code together)

• nephritic syndrome NOS (N05.-)

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 580.4 Acute glomerulonephritis with lesion of rapidly progressive glomerulonephritis (approximate)

Diagnosis Index entries for N01.1

• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › rapidly progressive › with › focal and segmental glomerular lesions

Nearby codes

• N01 Rapidly progressive nephritic syndrome
• N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality
• N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions (this code)
• N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
• N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
• N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
• N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
• N01.6 Rapidly progressive nephritic syndrome with dense deposit disease