N04.1 Nephrotic syndrome with focal and segmental glomerular lesions

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis.

Applicable to

• Nephrotic syndrome with focal and segmental hyalinosis
• Nephrotic syndrome with focal and segmental sclerosis
• Nephrotic syndrome with focal glomerulonephritis

Applies from N04 Nephrotic syndrome

Includes

• congenital nephrotic syndrome
• lipoid nephrosis

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 581.1 Nephrotic syndrome with lesion of membranous glomerulonephritis (approximate)

Code annotations containing back-references to N04.1

Back-references to N04

• Type 1 Excludes: Q63 Other congenital malformations of kidney ("congenital nephrotic syndrome (N04.-)")

Diagnosis Index entries for N04.1

• Nephrosis, nephrotic (Epstein's) (syndrome) (congenital) › with › glomerular lesion
• Syndrome › nephrotic (congenital) › with › focal and segmental glomerular lesions

Nearby codes

• N04 Nephrotic syndrome
• N04.0 Nephrotic syndrome with minor glomerular abnormality
• N04.1 Nephrotic syndrome with focal and segmental glomerular lesions (this code)
• N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis
• N04.20 Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
• N04.21 Primary membranous nephropathy with nephrotic syndrome
• N04.22 Secondary membranous nephropathy with nephrotic syndrome
• N04.29 Other nephrotic syndrome with diffuse membranous glomerulonephritis