N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions

Billable ICD-10-CM code, FY2026.

Applicable to

• Hereditary nephropathy, not elsewhere classified with focal and segmental hyalinosis
• Hereditary nephropathy, not elsewhere classified with focal and segmental sclerosis
• Hereditary nephropathy, not elsewhere classified with focal glomerulonephritis

Applies from N07 Hereditary nephropathy, not elsewhere classified

Excludes2 (not included here)

• Alport's syndrome (Q87.81-)
• hereditary amyloid nephropathy (E85.-)
• nail patella syndrome (Q87.2)
• non-neuropathic heredofamilial amyloidosis (E85.-)

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 583.89 Nephritis and nephropathy, not specified as acute or chronic, with other specified pathological lesion in kidney (approximate)

Diagnosis Index entries for N07.1

• Nephropathy › hereditary NEC › with › focal and segmental glomerular lesions

Nearby codes

• N07 Hereditary nephropathy, not elsewhere classified
• N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
• N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions (this code)
• N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
• N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
• N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
• N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
• N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease