P78.81 Congenital cirrhosis (of liver)

Billable ICD-10-CM code, FY2026.

Applies from P78 Other perinatal digestive system disorders

Excludes1 (never code together)

• cystic fibrosis (E84.0-E84.9)
• neonatal gastrointestinal hemorrhages (P54.0-P54.3)

MS-DRG index

Defines the logic of DRG(s) 794 in MDC 15.

Approximate ICD-9-CM (GEMs)

• 777.8 Other specified perinatal disorders of digestive system (approximate)

Code annotations containing back-references to P78.81

Back-references to P78.81

• Type 1 Excludes: K74 Fibrosis and cirrhosis of liver ("congenital cirrhosis (of liver) (P78.81)")
• Code First: P91.811 Neonatal encephalopathy in diseases classified elsewhere ("congenital cirrhosis (of liver) (P78.81)")

Diagnosis Index entries for P78.81

• Cirrhosis, cirrhotic (hepatic) (liver) › liver › congenital

Nearby codes

• P78.0 Perinatal intestinal perforation
• P78.1 Other neonatal peritonitis
• P78.2 Neonatal hematemesis and melena due to swallowed maternal blood
• P78.3 Noninfective neonatal diarrhea
• P78.8 Other specified perinatal digestive system disorders
• P78.81 Congenital cirrhosis (of liver) (this code)
• P78.82 Peptic ulcer of newborn
• P78.83 Newborn esophageal reflux
• P78.84 Gestational alloimmune liver disease
• P78.89 Other specified perinatal digestive system disorders
• P78.9 Perinatal digestive system disorder, unspecified