Q00.1 Craniorachischisis

Billable ICD-10-CM code, FY2026. Acts as a Major Complication or Comorbidity (MCC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Risk adjustment (HCC)

• CMS-HCC V28: HCC 182 — Spinal Cord Disorders/Injuries
• CMS-HCC V22: HCC 72 — Spinal Cord Disorders/Injuries
• RxHCC V08: HCC 155 — Spinal Cord Disorders
• ESRD V24: HCC 72

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 740.1 Craniorachischisis

Code annotations containing back-references to Q00.1

Back-references to Q00

• Type 2 Excludes: P04 Newborn affected by noxious substances transmitted via placenta or breast milk ("congenital malformations (Q00-Q99)")

Diagnosis Index entries for Q00.1

• Craniorachischisis (totalis)

Nearby codes

• Q00 Anencephaly and similar malformations
• Q00.0 Anencephaly
• Q00.1 Craniorachischisis (this code)
• Q00.2 Iniencephaly