Q04.9 Congenital malformation of brain, unspecified
Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.
Applicable to
- Congenital anomaly NOS of brain
- Congenital deformity NOS of brain
- Congenital disease or lesion NOS of brain
- Multiple anomalies NOS of brain, congenital
Applies from Q04 Other congenital malformations of brain
Excludes1 (never code together)
- cyclopia (Q87.0)
- macrocephaly (Q75.3)
Risk adjustment (HCC)
- CMS-HCC V28: HCC 182 — Spinal Cord Disorders/Injuries
- CMS-HCC V22: HCC 72 — Spinal Cord Disorders/Injuries
- RxHCC V08: HCC 155 — Spinal Cord Disorders
- ESRD V24: HCC 72
MS-DRG index
Defines the logic of DRG(s) 091-093 in MDC 01.
Approximate ICD-9-CM (GEMs)
742.9 Unspecified congenital anomaly of brain, spinal cord, and nervous system (approximate)
Diagnosis Index entries for Q04.9
- Anomaly, anomalous (congenital) (unspecified type) › brain (multiple)
- Anomaly, anomalous (congenital) (unspecified type) › cerebral
- Anomaly, anomalous (congenital) (unspecified type) › dura (brain)
- Cyclencephaly
- Deformity › brain (congenital)
- Deformity › cerebral, acquired › congenital
- Disease, diseased › brain › congenital
- Distortion (s) (congenital) › brain
- Lesion (s) (nontraumatic) › brain › congenital
- Malformation (congenital) › brain (multiple)
- Malformation (congenital) › cerebral
- Malformation (congenital) › dura › brain
Nearby codes
Q04.3 Other reduction deformities of brainQ04.4 Septo-optic dysplasia of brainQ04.5 MegalencephalyQ04.6 Congenital cerebral cystsQ04.8 Other specified congenital malformations of brainQ04.9 Congenital malformation of brain, unspecified (this code)