Q05.4 Unspecified spina bifida with hydrocephalus

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applies from Q05 Spina bifida

Includes

• hydromeningocele (spinal)
• meningocele (spinal)
• meningomyelocele
• myelocele
• myelomeningocele
• rachischisis
• spina bifida (aperta)(cystica)
• syringomyelocele

Excludes1 (never code together)

• Arnold-Chiari syndrome, type II (Q07.0-)
• spina bifida occulta (Q76.0)

Use additional code

• code for any associated paraplegia (paraparesis) (G82.2-)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 182 — Spinal Cord Disorders/Injuries
• CMS-HCC V22: HCC 72 — Spinal Cord Disorders/Injuries
• RxHCC V08: HCC 155 — Spinal Cord Disorders
• ESRD V24: HCC 72

MS-DRG index

Defines the logic of DRG(s) 091-093 in MDC 01.

Approximate ICD-9-CM (GEMs)

• 741.00 Spina bifida with hydrocephalus, unspecified region (approximate)

Code annotations containing back-references to Q05.4

Back-references to Q05.4

• Type 1 Excludes: Q03 Congenital hydrocephalus ("hydrocephalus with spina bifida (Q05.0-Q05.4)")

Back-references to Q05

• Type 1 Excludes: G91 Hydrocephalus ("spina bifida with hydrocephalus (Q05.-)")
• Type 1 Excludes: Q76.0 Spina bifida occulta ("meningocele (spinal) (Q05.-)")
• Type 1 Excludes: Q76.0 Spina bifida occulta ("spina bifida (aperta) (cystica) (Q05.-)")

Diagnosis Index entries for Q05.4

• Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent) › congenital (external) (internal) › with spina bifida
• Spina bifida (aperta) › with hydrocephalus NEC

Nearby codes

• Q05 Spina bifida
• Q05.0 Cervical spina bifida with hydrocephalus
• Q05.1 Thoracic spina bifida with hydrocephalus
• Q05.2 Lumbar spina bifida with hydrocephalus
• Q05.3 Sacral spina bifida with hydrocephalus
• Q05.4 Unspecified spina bifida with hydrocephalus (this code)
• Q05.5 Cervical spina bifida without hydrocephalus
• Q05.6 Thoracic spina bifida without hydrocephalus
• Q05.7 Lumbar spina bifida without hydrocephalus
• Q05.8 Sacral spina bifida without hydrocephalus
• Q05.9 Spina bifida, unspecified