Q13.81 Rieger anomaly

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Axenfeld-Rieger syndrome

Use additional code

• code for associated glaucoma (H42)

Code also

• any other associated congenital malformations such as cardiac defects

MS-DRG index

Defines the logic of DRG(s) 124-125 in MDC 02.

Approximate ICD-9-CM (GEMs)

• 743.44 Specified congenital anomalies of anterior chamber, chamber angle, and related structures (approximate)

Code annotations containing back-references to Q13.81

Back-references to Q13.81

• Code First: H42 Glaucoma in diseases classified elsewhere ("Rieger anomaly (Q13.81)")

Back-references to Q13.8

• Type 1 Excludes: H21.4 Pupillary membranes ("congenital pupillary membranes (Q13.8)")

Diagnosis Index entries for Q13.81

• Anomaly, anomalous (congenital) (unspecified type) › Rieger
• Glaucoma › in (due to) › Rieger anomaly
• Rieger anomaly or syndrome
• Syndrome › Axenfeld-Rieger

Nearby codes

• Q13.2 Other congenital malformations of iris
• Q13.3 Congenital corneal opacity
• Q13.4 Other congenital corneal malformations
• Q13.5 Blue sclera
• Q13.8 Other congenital malformations of anterior segment of eye
• Q13.81 Rieger anomaly (this code)
• Q13.89 Other congenital malformations of anterior segment of eye
• Q13.9 Congenital malformation of anterior segment of eye, unspecified