Q14.1 Congenital malformation of retina

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital retinal aneurysm

Applies from Q14 Congenital malformations of posterior segment of eye

Excludes2 (not included here)

• optic nerve hypoplasia (H47.03-)

MS-DRG index

Defines the logic of DRG(s) 124-125 in MDC 02.

Approximate ICD-9-CM (GEMs)

• 743.56 Other retinal changes, congenital (approximate)

Code annotations containing back-references to Q14.1

Back-references to Q14.1

• Type 1 Excludes: H33.1 Retinoschisis and retinal cysts ("congenital retinoschisis (Q14.1)")
• Type 2 Excludes: Q27 Other congenital malformations of peripheral vascular system ("congenital retinal aneurysm (Q14.1)")
• Type 2 Excludes: Q28 Other congenital malformations of circulatory system ("congenital retinal aneurysm (Q14.1)")

Diagnosis Index entries for Q14.1

• Aberrant (congenital) › artery (peripheral) › retina
• Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) › congenital (peripheral) › retina
• Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) › retina › congenital
• Anomaly, anomalous (congenital) (unspecified type) › artery (peripheral) › retina
• Anomaly, anomalous (congenital) (unspecified type) › fovea centralis
• Anomaly, anomalous (congenital) (unspecified type) › retina
• Aplasia › fovea centralis (congenital)
• Displacement, displaced › macula (congenital)
• Dysplasia › retinal, congenital
• Hypoplasia, hypoplastic › artery (peripheral) › retinal (congenital)
• Imperfect › closure (congenital) › retina
• Malformation (congenital) › retina
• Medullated fibers › retina
• Pigmentation (abnormal) (anomaly) › retina, congenital (grouped) (nevoid)
• Retinoschisis › congenital
• Stricture › artery › congenital (peripheral) › retinal
• Tortuous › retinal vessel, congenital

Nearby codes

• Q14 Congenital malformations of posterior segment of eye
• Q14.0 Congenital malformation of vitreous humor
• Q14.1 Congenital malformation of retina (this code)
• Q14.2 Congenital malformation of optic disc
• Q14.3 Congenital malformation of choroid
• Q14.8 Other congenital malformations of posterior segment of eye
• Q14.9 Congenital malformation of posterior segment of eye, unspecified