Q16.5 Congenital malformation of inner ear

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital anomaly of membranous labyrinth
• Congenital anomaly of organ of Corti

Applies from Q16 Congenital malformations of ear causing impairment of hearing

Excludes1 (never code together)

• congenital deafness (H90.-)

MS-DRG index

Defines the logic of DRG(s) 154-156 in MDC 03.

Approximate ICD-9-CM (GEMs)

• 744.05 Anomalies of inner ear

Code annotations containing back-references to Q16.5

Back-references to Q16.5

• Type 1 Excludes: Q17 Other congenital malformations of ear ("congenital malformations of ear with impairment of hearing (Q16.0-Q16.9)")

Diagnosis Index entries for Q16.5

• Absence (of) (organ or part) (complete or partial) › ear, congenital › inner
• Absence (of) (organ or part) (complete or partial) › inner ear, congenital
• Absence (of) (organ or part) (complete or partial) › labyrinth, membranous
• Absence (of) (organ or part) (complete or partial) › organ › of Corti, congenital
• Agenesis › labyrinth, membranous
• Agenesis › organ › of Corti
• Anomaly, anomalous (congenital) (unspecified type) › ear (external) › inner
• Anomaly, anomalous (congenital) (unspecified type) › labyrinth, membranous
• Anomaly, anomalous (congenital) (unspecified type) › organ › of Corti
• Aplasia › labyrinth, membranous
• Collapse › labyrinth, membranous (congenital)
• Deformity › ear (acquired) › congenital (external) › internal
• Deformity › organ of Corti (congenital)
• Degeneration, degenerative › membranous labyrinth, congenital (causing impairment of hearing)
• Degeneration, degenerative › saccule, congenital (causing impairment of hearing)
• Dilatation › saccule, congenital
• Distortion (s) (congenital) › ear (auricle) (external) › inner
• Distortion (s) (congenital) › organ › of Corti
• Enlargement, enlarged › vestibular aqueduct
• Malformation (congenital) › cochlea
• Malformation (congenital) › ear › inner
• Malformation (congenital) › internal ear
• Malformation (congenital) › Mondini's (congenital) (malformation, cochlea)
• Mondini's malformation (cochlea)

Nearby codes

• Q16.0 Congenital absence of (ear) auricle
• Q16.1 Congenital absence, atresia and stricture of auditory canal (external)
• Q16.2 Absence of eustachian tube
• Q16.3 Congenital malformation of ear ossicles
• Q16.4 Other congenital malformations of middle ear
• Q16.5 Congenital malformation of inner ear (this code)
• Q16.9 Congenital malformation of ear causing impairment of hearing, unspecified