Q26.0 Congenital stenosis of vena cava

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital stenosis of vena cava (inferior)(superior)

Risk adjustment (HCC)

• RxHCC V08: HCC 191 — Ventricular Septal Defect and Major Congenital Heart Disorders

MS-DRG index

Defines the logic of DRG(s) 306-307 in MDC 05.

Approximate ICD-9-CM (GEMs)

• 747.49 Other anomalies of great veins (approximate)

Code annotations containing back-references to Q26.0

Back-references to Q26

• Code Also: I27.21 Secondary pulmonary arterial hypertension ("congenital heart disease (Q20-Q28)")
• Type 2 Excludes: P29 Cardiovascular disorders originating in the perinatal period ("congenital malformations of the circulatory system (Q20-Q28)")
• Code Also: Z71.87 Encounter for pediatric-to-adult transition counseling ("congenital malformations of the circulatory system (Q20-Q28)")

Diagnosis Index entries for Q26.0

• Malformation (congenital) › great › vein › vena cava stenosis, congenital
• Stenosis, stenotic (cicatricial) › vena cava (inferior) (superior) › congenital
• Stricture › vena cava (inferior) (superior) NEC › congenital

Nearby codes

• Q26 Congenital malformations of great veins
• Q26.0 Congenital stenosis of vena cava (this code)
• Q26.1 Persistent left superior vena cava
• Q26.2 Total anomalous pulmonary venous connection
• Q26.3 Partial anomalous pulmonary venous connection
• Q26.4 Anomalous pulmonary venous connection, unspecified
• Q26.5 Anomalous portal venous connection