Q33.0 Congenital cystic lung

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital cystic lung disease
• Congenital honeycomb lung
• Congenital polycystic lung disease

Excludes1 (never code together)

• cystic fibrosis (E84.0)
• cystic lung disease, acquired or unspecified (J98.4)

MS-DRG index

Defines the logic of DRG(s) 205-206 in MDC 04.

Approximate ICD-9-CM (GEMs)

• 748.4 Congenital cystic lung

Code annotations containing back-references to Q33.0

Back-references to Q33

• Code Also: P28 Other respiratory conditions originating in the perinatal period (", if applicable, congenital malformations of the respiratory system (Q30-Q34)")

Diagnosis Index entries for Q33.0

• Cyst (colloid) (mucous) (simple) (retention) › bronchogenic (mediastinal) (sequestration) › congenital
• Cyst (colloid) (mucous) (simple) (retention) › congenital NEC › lung
• Cyst (colloid) (mucous) (simple) (retention) › lung › congenital
• Cystic › lung disease › congenital
• Disease, diseased › cystic › lung › congenital
• Disease, diseased › lung › cystic › congenital
• Disease, diseased › lung › polycystic › congenital
• Disease, diseased › polycystic › lung or pulmonary › congenital
• Honeycomb lung › congenital
• Polycystic (disease) › lung › congenital

Nearby codes

• Q33 Congenital malformations of lung
• Q33.0 Congenital cystic lung (this code)
• Q33.1 Accessory lobe of lung
• Q33.2 Sequestration of lung
• Q33.3 Agenesis of lung
• Q33.4 Congenital bronchiectasis
• Q33.5 Ectopic tissue in lung