Q38.0 Congenital malformations of lips, not elsewhere classified

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital fistula of lip
• Congenital malformation of lip NOS
• Van der Woude's syndrome

Excludes1 (never code together)

• cleft lip (Q36.-)
• cleft lip with cleft palate (Q37.-)
• macrocheilia (Q18.6)
• microcheilia (Q18.7)

Applies from Q38 Other congenital malformations of tongue, mouth and pharynx

Excludes1 (never code together)

• dentofacial anomalies (M26.-)
• macrostomia (Q18.4)
• microstomia (Q18.5)

MS-DRG index

Defines the logic of DRG(s) 011-013 in MDC PRE.

Approximate ICD-9-CM (GEMs)

• 750.25 Congenital fistula of lip (approximate)

Code annotations containing back-references to Q38.0

Back-references to Q38.0

• Type 1 Excludes: K13.0 Diseases of lips ("congenital fistula of lips (Q38.0)")

Diagnosis Index entries for Q38.0

• Agenesis › lip
• Anomaly, anomalous (congenital) (unspecified type) › lip
• Deformity › lip (acquired) NEC › congenital
• Ectropion › lip (acquired) › congenital
• Fistula (cutaneous) › lip › congenital
• Malformation (congenital) › lip
• Van der Woude's syndrome

Nearby codes

• Q38 Other congenital malformations of tongue, mouth and pharynx
• Q38.0 Congenital malformations of lips, not elsewhere classified (this code)
• Q38.1 Ankyloglossia
• Q38.2 Macroglossia
• Q38.3 Other congenital malformations of tongue
• Q38.4 Congenital malformations of salivary glands and ducts
• Q38.5 Congenital malformations of palate, not elsewhere classified