Q40.0 Congenital hypertrophic pyloric stenosis

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Congenital or infantile constriction
• Congenital or infantile hypertrophy
• Congenital or infantile spasm
• Congenital or infantile stenosis
• Congenital or infantile stricture

Risk adjustment (HCC)

• CMS-HCC V28: HCC 78 — Intestinal Obstruction/Perforation

MS-DRG index

Defines the logic of DRG(s) 393-395 in MDC 06.

Approximate ICD-9-CM (GEMs)

• 750.5 Congenital hypertrophic pyloric stenosis

Code annotations containing back-references to Q40.0

Back-references to Q40.0

• Type 1 Excludes: K31.1 Adult hypertrophic pyloric stenosis ("congenital or infantile pyloric stenosis (Q40.0)")
• Type 1 Excludes: K31.3 Pylorospasm, not elsewhere classified ("congenital or infantile pylorospasm (Q40.0)")

Diagnosis Index entries for Q40.0

• Achalasia (cardia) (esophagus) › pylorus
• Constriction › pylorus (adult hypertrophic) › congenital or infantile
• Constriction › pylorus (adult hypertrophic) › newborn
• Hypertrophy, hypertrophic › pylorus (adult) (muscle) (sphincter) › congenital or infantile
• Obstruction, obstructed, obstructive › pylorus › congenital or infantile
• Pylorospasm (reflex) NEC › congenital or infantile
• Pylorospasm (reflex) NEC › newborn
• Spasm (s), spastic, spasticity › pylorus NEC › congenital or infantile
• Stenosis, stenotic (cicatricial) › pylorus (hypertrophic) (acquired) › congenital
• Stenosis, stenotic (cicatricial) › pylorus (hypertrophic) (acquired) › infantile
• Stricture › pylorus (hypertrophic) › congenital
• Stricture › pylorus (hypertrophic) › infantile

Nearby codes

• Q40 Other congenital malformations of upper alimentary tract
• Q40.0 Congenital hypertrophic pyloric stenosis (this code)
• Q40.1 Congenital hiatus hernia
• Q40.2 Other specified congenital malformations of stomach
• Q40.3 Congenital malformation of stomach, unspecified
• Q40.8 Other specified congenital malformations of upper alimentary tract
• Q40.9 Congenital malformation of upper alimentary tract, unspecified