Q41.1 Congenital absence, atresia and stenosis of jejunum

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Apple peel syndrome
• Imperforate jejunum

Applies from Q41 Congenital absence, atresia and stenosis of small intestine

Includes

• congenital obstruction, occlusion or stricture of small intestine or intestine NOS

Excludes1 (never code together)

• cystic fibrosis with intestinal manifestation (E84.11)
• meconium ileus NOS (without cystic fibrosis) (P76.0)

Risk adjustment (HCC)

• CMS-HCC V28: HCC 78 — Intestinal Obstruction/Perforation

MS-DRG index

Defines the logic of DRG(s) 393-395 in MDC 06.

Approximate ICD-9-CM (GEMs)

• 751.1 Atresia and stenosis of small intestine (approximate)

Code annotations containing back-references to Q41.1

Back-references to Q41

• Type 1 Excludes: K56 Paralytic ileus and intestinal obstruction without hernia ("congenital stricture or stenosis of intestine (Q41-Q42)")

Diagnosis Index entries for Q41.1

• Absence (of) (organ or part) (complete or partial) › jejunum (acquired) › congenital
• Agenesis › jejunum
• Anomaly, anomalous (congenital) (unspecified type) › apple peel syndrome
• Apple peel syndrome
• Atresia, atretic › jejunum
• Imperforate (congenital) › jejunum
• Stenosis, stenotic (cicatricial) › jejunum › congenital
• Stricture › jejunum › congenital

Nearby codes

• Q41 Congenital absence, atresia and stenosis of small intestine
• Q41.0 Congenital absence, atresia and stenosis of duodenum
• Q41.1 Congenital absence, atresia and stenosis of jejunum (this code)
• Q41.2 Congenital absence, atresia and stenosis of ileum
• Q41.8 Congenital absence, atresia and stenosis of other specified parts of small intestine
• Q41.9 Congenital absence, atresia and stenosis of small intestine, part unspecified