Q43.1 Hirschsprung's disease

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Aganglionosis
• Congenital (aganglionic) megacolon

Risk adjustment (HCC)

• CMS-HCC V28: HCC 78 — Intestinal Obstruction/Perforation

MS-DRG index

Defines the logic of DRG(s) 393-395 in MDC 06.

Approximate ICD-9-CM (GEMs)

• 751.3 Hirschsprung's disease and other congenital functional disorders of colon (approximate)

Code annotations containing back-references to Q43.1

Back-references to Q43.1

• Type 1 Excludes: K59.3 Megacolon, not elsewhere classified ("congenital megacolon (aganglionic) (Q43.1)")
• Type 1 Excludes: K59.3 Megacolon, not elsewhere classified ("megacolon (due to) (in) Hirschsprung's disease (Q43.1)")
• Type 1 Excludes: P76.1 Transitory ileus of newborn ("Hirschsprung's disease (Q43.1)")

Diagnosis Index entries for Q43.1

• Aganglionosis (bowel) (colon)
• Dilatation › colon › congenital
• Hirschsprung's disease or megacolon
• Ileus (bowel) (colon) (inhibitory) (intestine) › neurogenic › Hirschsprung's disease or megacolon
• Macrocolon
• Megacolon (acquired) (functional) (not Hirschsprung's disease) (in) › congenital, congenitum (aganglionic)
• Megacolon (acquired) (functional) (not Hirschsprung's disease) (in) › Hirschsprung's (disease)
• Obstruction, obstructed, obstructive › intestine › neurogenic › Hirschsprung's disease or megacolon

Nearby codes

• Q43 Other congenital malformations of intestine
• Q43.0 Meckel's diverticulum (displaced) (hypertrophic)
• Q43.1 Hirschsprung's disease (this code)
• Q43.2 Other congenital functional disorders of colon
• Q43.3 Congenital malformations of intestinal fixation
• Q43.4 Duplication of intestine
• Q43.5 Ectopic anus
• Q43.6 Congenital fistula of rectum and anus