Q44.71 Alagille syndrome

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applicable to

• Alagille-Watson syndrome

Applies from Q44.7 Other congenital malformations of liver

Code also

• , if applicable, associated malformations affecting other systems

Risk adjustment (HCC)

• CMS-HCC V28: HCC 68 — Cholangitis and Obstruction of Bile Duct Without Gallstones

MS-DRG index

Defines the logic of DRG(s) 441-443 in MDC 07.

Diagnosis Index entries for Q44.71

• Alagille (-Watson) syndrome
• Syndrome › Alagille (-Watson)

Nearby codes

• Q44.4 Choledochal cyst
• Q44.5 Other congenital malformations of bile ducts
• Q44.6 Cystic disease of liver
• Q44.7 Other congenital malformations of liver
• Q44.70 Other congenital malformation of liver, unspecified
• Q44.71 Alagille syndrome (this code)
• Q44.79 Other congenital malformations of liver