Q56.1 Male pseudohermaphroditism, not elsewhere classified

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• 46, XY with streak gonads
• Male pseudohermaphroditism NOS

Applies from Q56 Indeterminate sex and pseudohermaphroditism

Excludes1 (never code together)

• 46,XX true hermaphrodite (Q99.1)
• androgen insensitivity syndrome (E34.5-)
• chimera 46,XX/46,XY true hermaphrodite (Q99.0)
• female pseudohermaphroditism with adrenocortical disorder (E25.-)
• pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
• pure gonadal dysgenesis (Q99.1)

MS-DRG index

Defines the logic of DRG(s) 729-730 in MDC 12.

Approximate ICD-9-CM (GEMs)

• 752.7 Indeterminate sex and pseudohermaphroditism (approximate)

Code annotations containing back-references to Q56.1

Back-references to Q56

• Type 1 Excludes: E25 Adrenogenital disorders ("indeterminate sex and pseudohermaphroditism (Q56)")

Diagnosis Index entries for Q56.1

• Karyotype › 46,XY › with streak gonads
• Pseudohermaphroditism › male
• Pseudohermaphroditism › male › with › cleft scrotum
• Pseudohermaphroditism › male › without gonadal disorder
• Rudimentary (congenital) › uterus › in male

Nearby codes

• Q56 Indeterminate sex and pseudohermaphroditism
• Q56.0 Hermaphroditism, not elsewhere classified
• Q56.1 Male pseudohermaphroditism, not elsewhere classified (this code)
• Q56.2 Female pseudohermaphroditism, not elsewhere classified
• Q56.3 Pseudohermaphroditism, unspecified
• Q56.4 Indeterminate sex, unspecified