Q61.19 Other polycystic kidney, infantile type

Billable ICD-10-CM code, FY2026. Acts as a Complication or Comorbidity (CC) as a secondary diagnosis. Exempt from present-on-admission (POA) reporting.

Applies from Q61 Cystic kidney disease

Excludes1 (never code together)

• acquired cyst of kidney (N28.1)
• Potter's syndrome (Q60.6)

Applies from Q61.1 Polycystic kidney, infantile type

Applicable to

• Polycystic kidney, autosomal recessive

MS-DRG index

Defines the logic of DRG(s) 698-700 in MDC 11.

Approximate ICD-9-CM (GEMs)

• 753.14 Polycystic kidney, autosomal recessive (approximate)

Code annotations containing back-references to Q61.19

Back-references to Q61

• Type 1 Excludes: N28.1 Cyst of kidney, acquired ("cystic kidney disease (congenital) (Q61.-)")

Diagnosis Index entries for Q61.19

• Cyst (colloid) (mucous) (simple) (retention) › congenital NEC › kidney › more than one (multiple) › specified as polycystic › infantile type NEC
• Cyst (colloid) (mucous) (simple) (retention) › kidney › more than one (multiple) › specified as polycystic › infantile type (autosomal recessive) NEC
• Cystic › kidney (congenital) › infantile type NEC
• Degeneration, degenerative › kidney › polycystic › infantile type (autosomal recessive) NEC
• Disease, diseased › kidney (functional) (pelvis) › polycystic › childhood type NEC
• Disease, diseased › polycystic › kidney or renal › childhood type NEC
• Disease, diseased › renal (functional) (pelvis) › polycystic (congenital) › childhood type NEC
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › polycystic › autosomal › recessive NEC
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › polycystic › childhood type NEC
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › polycystic › infantile type NEC
• Polycystic (disease) › degeneration, kidney › autosomal recessive (infantile type) NEC
• Polycystic (disease) › kidney › autosomal › recessive NEC
• Polycystic (disease) › kidney › autosomal recessive (childhood type) NEC
• Polycystic (disease) › kidney › infantile type NEC

Nearby codes

• Q61.00 Congenital renal cyst, unspecified
• Q61.01 Congenital single renal cyst
• Q61.02 Congenital multiple renal cysts
• Q61.1 Polycystic kidney, infantile type
• Q61.11 Cystic dilatation of collecting ducts
• Q61.19 Other polycystic kidney, infantile type (this code)
• Q61.2 Polycystic kidney, adult type
• Q61.3 Polycystic kidney, unspecified
• Q61.4 Renal dysplasia
• Q61.5 Medullary cystic kidney
• Q61.8 Other cystic kidney diseases