Q76.1 Klippel-Feil syndrome

Billable ICD-10-CM code, FY2026. Exempt from present-on-admission (POA) reporting.

Applicable to

• Cervical fusion syndrome

Applies from Q76 Congenital malformations of spine and bony thorax

Excludes1 (never code together)

• congenital musculoskeletal deformities of spine and chest (Q67.5-Q67.8)

MS-DRG index

Defines the logic of DRG(s) 564-566 in MDC 08.

Approximate ICD-9-CM (GEMs)

• 756.16 Klippel-Feil syndrome

Code annotations containing back-references to Q76.1

Back-references to Q76.1

• Type 1 Excludes: M43 Other deforming dorsopathies ("Klippel-Feil syndrome (Q76.1)")

Back-references to Q76

• Type 1 Excludes: M24.3 Pathological dislocation of joint, not elsewhere classified ("congenital dislocation or displacement of joint- see congenital malformations and deformations of the musculoskeletal system (Q65-Q79)")
• Type 2 Excludes: M95 Other acquired deformities of musculoskeletal system and connective tissue ("congenital malformations and deformations of the musculoskeletal system (Q65-Q79)")

Diagnosis Index entries for Q76.1

• Anomaly, anomalous (congenital) (unspecified type) › Klippel-Feil (brevicollis)
• Cervical › fusion syndrome
• Deformity › Klippel-Feil (brevicollis)
• Disease, diseased › Klippel-Feil (brevicollis)
• Feil-Klippel syndrome (brevicollis)
• Klippel-Feil deficiency, disease, or syndrome (brevicollis)
• Syndrome › cervical (root) › fusion
• Syndrome › Feil-Klippel (brevicollis)
• Syndrome › Klippel-Feil (brevicollis)

Nearby codes

• Q76 Congenital malformations of spine and bony thorax
• Q76.0 Spina bifida occulta
• Q76.1 Klippel-Feil syndrome (this code)
• Q76.2 Congenital spondylolisthesis
• Q76.3 Congenital scoliosis due to congenital bony malformation
• Q76.4 Other congenital malformations of spine, not associated with scoliosis
• Q76.41 Congenital kyphosis
• Q76.411 Congenital kyphosis, occipito-atlanto-axial region